<110>    NovaZyme Inc.

<120>    Composition for treating Glutaric aciduria and administrating
         method thereof

<130>    FC20104WO

<160>    2

<170>    KoPatentIn 3.0

<210>    1
<211>    438
<212>    PRT
<213>    homo sapiens

<400>    1
Met Ala Leu Arg Gly Val Ser Val Arg Leu Leu Ser Arg Gly Pro Gly
  1               5                  10                  15 

Leu His Val Leu Arg Thr Trp Val Ser Ser Ala Ala Gln Thr Glu Lys
             20                  25                  30 

Gly Gly Arg Thr Gln Ser Gln Leu Ala Lys Ser Ser Arg Pro Glu Phe
         35                  40                  45 

Asp Trp Gln Asp Pro Leu Val Leu Glu Glu Gln Leu Thr Thr Asp Glu
     50                  55                  60 

Ile Leu Ile Arg Asp Thr Phe Arg Thr Tyr Cys Gln Glu Arg Leu Met
 65                  70                  75                  80 

Pro Arg Ile Leu Leu Ala Asn Arg Asn Glu Val Phe His Arg Glu Ile
                 85                  90                  95 

Ile Ser Glu Met Gly Glu Leu Gly Val Leu Gly Pro Thr Ile Lys Gly
            100                 105                 110 

Tyr Gly Cys Ala Gly Val Ser Ser Val Ala Tyr Gly Leu Leu Ala Arg
        115                 120                 125 

Glu Leu Glu Arg Val Asp Ser Gly Tyr Arg Ser Ala Met Ser Val Gln
    130                 135                 140 

Ser Ser Leu Val Met His Pro Ile Tyr Ala Tyr Gly Ser Glu Glu Gln
145                 150                 155                 160 

Arg Gln Lys Tyr Leu Pro Gln Leu Ala Lys Gly Glu Leu Leu Gly Cys
                165                 170                 175 

Phe Gly Leu Thr Glu Pro Asn Ser Gly Ser Asp Pro Ser Ser Met Glu
            180                 185                 190 

Thr Arg Ala His Tyr Asn Ser Ser Asn Lys Ser Tyr Thr Leu Asn Gly
        195                 200                 205 

Thr Lys Thr Trp Ile Thr Asn Ser Pro Met Ala Asp Leu Phe Val Val
    210                 215                 220 

Trp Ala Arg Cys Glu Asp Gly Cys Ile Arg Gly Phe Leu Leu Glu Lys
225                 230                 235                 240 

Gly Met Arg Gly Leu Ser Ala Pro Arg Ile Gln Gly Lys Phe Ser Leu
                245                 250                 255 

Arg Ala Ser Ala Thr Gly Met Ile Ile Met Asp Gly Val Glu Val Pro
            260                 265                 270 

Glu Glu Asn Val Leu Pro Gly Ala Ser Ser Leu Gly Gly Pro Phe Gly
        275                 280                 285 

Cys Leu Asn Asn Ala Arg Tyr Gly Ile Ala Trp Gly Val Leu Gly Ala
    290                 295                 300 

Ser Glu Phe Cys Leu His Thr Ala Arg Gln Tyr Ala Leu Asp Arg Met
305                 310                 315                 320 

Gln Phe Gly Val Pro Leu Ala Arg Asn Gln Leu Ile Gln Lys Lys Leu
                325                 330                 335 

Ala Asp Met Leu Thr Glu Ile Thr Leu Gly Leu His Ala Cys Leu Gln
            340                 345                 350 

Leu Gly Arg Leu Lys Asp Gln Asp Lys Ala Ala Pro Glu Met Val Ser
        355                 360                 365 

Leu Leu Lys Arg Asn Asn Cys Gly Lys Ala Leu Asp Ile Ala Arg Gln
    370                 375                 380 

Ala Arg Asp Met Leu Gly Gly Asn Gly Ile Ser Asp Glu Tyr His Val
385                 390                 395                 400 

Ile Arg His Ala Met Asn Leu Glu Ala Val Asn Thr Tyr Glu Gly Thr
                405                 410                 415 

His Asp Ile His Ala Leu Ile Leu Gly Arg Ala Ile Thr Gly Ile Gln
            420                 425                 430 

Ala Phe Thr Ala Ser Lys
        435            


<210>    2
<211>    19
<212>    PRT
<213>    Artificial Sequence

<220>
<223>    signal peptide


<400>    2
Glu Thr Asp Thr Leu Leu Leu Trp Val Leu Leu Leu Trp Val Pro Gly
  1               5                  10                  15 

Ser Thr Gly
           
